Since there is no compatible bone marrow donor, the prognosis of SCID is poor, and the purpose of care is to support the family to take care of deadly children. Genetic counseling is essential because of the spread of any form of the disease. The goal of care is to help parents prevent child infections, such as careful isolation of crowded facilities and active infections, careful skin and oral care, good general nutrition, and careful supervision during the activity to prevent skin trauma. However, even with strict environmental controls, these children are prone to opportunistic infections. Despite the positive efforts in prevention or treatment, chronic fungal infections of the oral cavity and nails of Candida albicans are a common problem.

The hoarseness may be caused by repeated esophageal and vocal cord erosion of the fungus. It is important to emphasize to parents that these conditions are not the result of their relaxation in preventing them, but the result of a serious immune disorder. Parents should be encouraged to immediately notify the doctor of any evidence of worsening infection.

Children who are regularly injected with serum serum globulin [ISG or IG] need support during surgery because the injection is painful. Infants are best comforted by their parents, but young children and preschoolers may benefit from acupuncture. Immunoglobulins are deeply injected into large muscle groups, usually the lateral femoral muscles. To prevent tissue damage and provide maximum absorption, the total amount can be divided into two injections and given at two different locations. Keep a record of these locations to ensure a rotation schedule for future injections. Intravenous formulations of ISG [Intravenous Modified ISG [MISG]] are available, which are reported to be more effective and cause less pain.

A rare complication of long-term ISG administration is the toxicity of mercury [gout or pink disease] caused by mercury-containing bacteriostatic agents in commercial preparations. Nurses working with these patients should be aware of signs of this unusual reaction, including pink, scaly itching of the palms and soles of the feet, photophobia, sweating, irritability and insomnia.

Care for patients undergoing bone marrow transplantation is primarily directed at preventing infection. Because the evidence of bone marrow function is clearly 7 to 20 days, the hospital stay is very long. The purpose of this discussion is not to describe in detail the care of bone marrow transplant patients, except for the professional care involved, which emphasizes that the psychological needs of parents and children are enormous. For parents, it represents the last hope for successful treatment and survival. For children, this means feeling deprivation, because isolation, massive blood tests, and more pain and pain if graft-versus-host response occurs. To meet these needs, a sensitive, consistent team of nurses is effective and as a member of the entire medical team is critical.

Nursing considerations for patients with severe combined immunodeficiency disease (SCID) was originally published on Spring